Primary Systemic Amyloidosis

Authors

  • Maria Syed Department of Dermatology. Pakistan Institute of Medical Sciences, Islamabad, Pakistan.
  • Afaq Ahmad Department of Dermatology. Pakistan Institute of Medical Sciences, Islamabad, Pakistan
  • Anwar Ul Haque Department of Pathology AJK Medical College, AJK University, Muzaffarabad, Azad Kashmir

Keywords:

Amyloidosis, Primary systemic amyloidosis, macroglossia, carpal tunnel syndrome, electrophoresis

Abstract

Primary systemic amyloidosis is a rare entity. We report a case of primary systemic amyloidosis without
any associated hematological abnormality who presented with macroglossia and hemorrhagic lesions around
eyes and sub mammary region. There were soft lobulated masses around perianal region, labia majora and on external
auditory meatus obstructing auditory canal. She was also operated for carpel tunnel syndrome in thepast.
Urine and serum electrophoresis were negative. Diagnosis was confirmed by biopsy of submammary skin lesion
using haematoxylin and eosin and Congo red stain. Polarized microscopy was used to see birefringence of amyloid.

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Published

2018-11-16

Issue

Volume.11, Issue (January-June, 2013)

Section

Original article

License

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How to Cite

1.
Syed M, Ahmad A, Haque AU. Primary Systemic Amyloidosis. Int J Pathol [Internet]. 2018 Nov. 16 [cited 2024 Nov. 24];:16-8. Available from: https://jpathology.com/index.php/OJS/article/view/128