Amira Niazi and Anwar Ul Haque
Department of Pathology, Pakistan Institute of Medical Sciences, Islamabad.
Alveolar soft part sarcoma is a rare neoplasm,
usually seen in young patients of < 30 years of age.There is an age range of 0- 74 years. Most of the patients are young females. It usually occurs inextremities specially thigh, buttock, oral cavity, pharynx including tongue, mediastinum, sometimes from pulmonary vein, stomach, retroperitonium,uterus, vagina, and orbit. It is a very vascular tumour and bruit is usually present. Local recurrence rate is 20-33%. This neoplasm is known to have late recurrences. Incidence of metastasis is 66%.1